|
KMID : 1141320200350010064
|
|
Kosin Medical Journal
2020 Volume.35 No. 1 p.64 ~ p.68
|
|
|
General Anesthesia for a Patient with GNE Myopathy: a case report
|
|
Kang Christine
An Ji-Hye
Kwon Jae-Young
Hwang Boo-Young
|
|
|
Abstract
|
|
|
|
GNE, or bifunctional UDP-N-acetylglucosamine 2-epimerase/N-acetylmannosamine kinase, myopathy presents withs ymptoms of foot drop, followed by lower and upper extremity muscle weaknesses and sparing of the quadriceps. Myopathies usually increase the risks of complications related to general anesthesia. The anesthetic management of patientsw ith GNEmyopathy has not been previously reported. Herein, we report a case of GNEmyopathy in a 37-year-old womana nd discuss anesthetic considerations for elective laparoscopic hysterectomy and bilateral salpingectomy, focusing on thep ostoperative airway management. We avoided administering neuromuscular-blocking agents and instead used a laryngeal mask airway. The anesthetic management combining the use of a laryngeal mask airway and desflurane without neuromuscular-blocking agents provided sufficient abdominal and diaphragmatic muscle relaxations for sustaining the pneumoperitoneum for lap aroscopic surgery.
|
|
|
KEYWORD
|
|
|
GNE myopathy, Laryngeal mask airway, Neuromuscular Blocking Agents
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
 
|